The aim of our study was to follow the evolution of phenotype for children with lattice corneal dystrophy type I and granular corneal dystrophy type I. Mean age was 8,84 ± 4,20 years and 17,78 ± 3,76 years respectively. Corneal parameters were analysed from Scheimpflug photographs: number of opacities, location, thickness, depth and percentage of corneal transparency. Peripheral opacities in LCDI children continued to increase when the number of central deposits tended to stagnate after a mean age of 12 ± 1 years. GCDI children presented a continuous increase in number of opacities. Our results show a phenotypic heterogeneity, especially in early ages, which can lead to misdiagnosis.