Pigmented Paravenous Retinochoroidal Atrophy

Abstract

ABSTRACT

Pigmented paravenous retinochoroidal atrophy is a rare disorder that is not well understood or classified. We examined a patient who had chorioretinal atrophy with pigment clusters located in the paravenous areas without macular involvement. Other conditions which may also present retinochoroidal atrophy and/or pigmentary degeneration are discussed. The electroretinography results were subnormal but the evoked potentials were not totally extinguished. Fluorescein angiography and retinography confirmed the relative and absolute scotomas corresponding to the atrophic paravenous areas.