Darier's disease is an autosomal dominant genodermatosis typified by hyperkeratotic papules and plaques in a predominately seborrheic distribution. The vesiculo-bullous variant of Darier's disease is rare. Several previously reported cases have demonstrated clinical and microscopic features resembling familial benign chronic pemphigus or Hailey-Hailey disease.Objectives:
The objective of this report is to describe an uncommon presentation of Darier's disease, which has been infrequently described in the literature.Methods:
The authors present a case of bullous flare of long-standing Darier's disease.Conclusions:
Darier's disease may assume several atypical morphologies, including vesiculo-bullous lesions.