to assess the frequency of clinical symptoms and physical examination signs, allowing to differentiate forms of pulmonary hypertension (IPAH - idiopathic pulmonary arterial hypertension, PAH due to CHD - congenital heart disease)Design and method:
We studied 70 patients with IPAH and 29 patients with PAH-CHDResults:
In patients with IPAH compared to patients with PAH-CHD were more frequent clinical symptoms - syncope, cough (p < 0,05). While in PAH-CHD- shortness of breath, fatigue(p < 0,05).Results:
Most often signs of the physical examination in IPAH were ankle oedema, accentuated pulmonary component of the second heart sound, lung crackels (p < 0,05). At the same time the most frequent finding in patients with CHD was cyanosis (Table 1)Conclusions:
Careful questioning of each PAH patient about the history of symptoms and signs, clinical examination may suggest an underlying cause of PAH at early stage of the disease.