Dermatofibrosarcoma Protuberans of the Vulva: Report of Two New Cases and Review of the Literature

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Abstract

Background

Dermatofibrosarcoma protuberans (DFSP), a low-grade sarcoma of dermal origin, rarely is found on the vulva. Only 16 cases of DFSP of the vulva have been described.

Cases

Two patients with long histories of primary vulvar dermatofibrosarcoma protuberans are presented. Both required multiple excisions to resect the tumor completely. The patients remain without evidence of disease after long-term follow-up. One patient is among the youngest recorded. All published cases of vulvar DFSP are reviewed.

Conclusions

Both our experience and that reported in previous cases indicate that wide local excision is required in the treatment of vulvar DFSP.

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