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Human prion diseases: Molecular, cellular and population biology
Localization of CHMP2B-immunoreactivity in the brainstem of Lewy body disease
Olig2-positive cells in glioneuronal tumors show both glial and neuronal characters: The implication of a common progenitor cell?
The contribution of HIV infection to intracranial arterial remodeling: A pilot study
Proteomics-based analysis of invasion-related proteins in malignant gliomas
Ultrastructural changes in LGMD1F
Giant cell polymyositis and myocarditis associated with myasthenia gravis and thymoma
A biphasic tumor consisting of pilocytic astrocytoma with an anaplastic solitary fibrous tumor component in the pineal region: A case report and literature review
Contiguous ABCD1 DXS1357E deletion syndrome: Report of an autopsy case
Immunohistochemical and molecular genetics study of a granular cell astrocytoma: A case report of malignant transformation to a glioblastoma
Central nervous system marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue type involving the brain and spinal cord parenchyma
Cerebral astroblastoma in an adult: An immunohistochemical, ultrastructural and genetic study
Extraosseous plasmacytoma with an aggressive course occurring solely in the CNS
Bilateral intraventricular mass in a child
The 40th Cliniconeuropathological Meeting 17–18 November 2012
Autopsy Consent, Brain Collection, and Standardized Neuropathologic Assessment of ADNI Participants: the Essential Role of the Neuropathology Core
The Role of Brain Histopathology in Neuro – PET and SPECT tracer Development
For the Establishment of Japanese Brain Bank Network
Efforts and Problems of Constructing Brain Banks for Psychiatric Research in Japan
Brain Banks and Target Discovery, Past, Present and Future
Genomics and Brain Bank
“Brain Disease Researches and Brain Bank”
The Dominantly Inherited Alzheimer Network (DIAN): the Essential Role of the Neuropathology Core
Definition and Differentials -How to Distinguish Disease-Specific Changes on Microscopy-
Distinguishing Between Argyrophilic Grains and Neutrophil Threads
Astrocytic inclusions of tauopathies -astrocytic plaque, tufted astrocyte, bush-like astrocyte and thorn shaped astrocyte-
Pretangles and Neurofibrillary Changes: Definitions and Differentials
The Classification of TDP-43 Pathology in Frontotemporal Lobar Degeneration: Its Significance and Limitation
Basophilic Inclusions and Neuronal Intermediate Filament Inclusions in Amyotrophic Lateral Sclerosis and Frontotemporal Lobar Degeneration
A 40-year-old woman with drug-resistant temporal lobe epilepsy
An 80-year-old case with gait disturbance showing high signal intensity in FLAIR and T2-weighted MR images in the brain stem and cerebellum
A left temporal lobe lesion of a 61-year-old male patient
A case of early onset dementia as depressive state at age 32 with chorea-like involuntary movement
A 59-year-old man with subacutely progressive muscle weakness of limb and trunk
Title: A 5-year-old girl who developed clubfoot during infancy
Neuropathology of Schizophrenia –past and future- ˜Is schizophrenia the graveyard of neuropathologists really? ˜
Technical considerations in pH measurement of postmortem brain tissues
Detection of cells with loss of cytochrome c oxidase in brain of mitochondrial disease –a comparative study in mice and human brain samples
Genetic Neuropathology: New Approach to the Study of Postmortem Brain in Psychiatric Illnesses
Periventricular nodular heterotopia functionally couples with the overlying hippocampus
Elucidation of the molecular functions and LOF of the CDKL5, a causative gene for neurodevelopmental disorders
The white matter lesion in xeroderma pigmentosum and Cockayne syndrome
Progressive multifocal leukoencephalopathy: Expression of cell cycle regulators and alteration of PML-NBs in the enlarging nuclei of glial cells
Possible pathogenic microorganism for trimethoprim-sulfamethoxazxole-responsive chronic encephalomyelitis: Histopathologic analysis of brain biopsy specimens from 4 cases
Analysis of the relationship between methyl CpG binding protein 2 and JC viral proteins
A rare case of cerebral amyloid angiopathy-related inflammation with an apolipoprotein E genotype of ε3/ε3
The role of Matrix metalloproteinases and effect of minocycline in EAE
The relationship between Aquaporin 4-related astrocytopathy and Aquaporin 1
Neuromyelitis optica spectrum disorders (NMOSD) without optic neuritis: an autopsy case
Degeneration of neurons and neuropils in Lysosome diseases
Immunohistochemical study on brains of two autopsy cases of adult-onset type 2 citrullinemia
Neuropathological study on the glial cells in brains of two autopsy cases of aceruloplasminemia
Trans-synaptic degenerations in human limbic system
Intracerebral localization of glucose transporter 5
Thalamic hemorrhage: its anatomical classification related to the arterial supply of the thalamus
Ubiquilin immunoreactivity in cytoplasmic and nuclear inclusions in synucleinopathies, polyglutamine diseases and intranuclear inclusion body disease
Valosin-containing protein immunoreactivity in tauopathies, synucleinopathies, polyglutamine diseases and intranuclear inclusion body disease
Localization of Keap1 in cytoplasmic inclusions in various neurodegenerative diseases
Frequency of ballooned neurons in amygdala: a comparison between corticobasal degeneration and argyrophilic grain disease
TDP-43 in the cerebral cortex of sporadic amyotrophic lateral sclerosis: histological and biochemical analysis
Immunohistochemical analysis of the cerebellum in amyotrophic lateral screlosis (ALS)/parkinson-dementia complex (PDC) in Kii peninsula (Kii ALS/PDC, Muro disease)
Bunina bodies and molecular chaperone
Xanthine oxidoreductase (XOR) inhibitors that are not substrates for the purine salvage pathway suppress ALS progression
Influence of SOD1 mutation on astrocytic MCP-1/CCR2 signaling
Relationship between soluble iron accumulation and glutamate metabolism in amyotrophic lateral sclerosis
Additional immunohistochemical examination of 14-3-3 protein seven isoforms in amyotrophic lateral sclerosis
Immunohistochemical study on ESCRT (endosomal sorting complex required for transport)-related molecules in the spinal cord of sporadic amyotrophic lateral sclerosis (SALS)
XIAP is localized in inclusion bodies in ALS
Adenovirus-, lentivirus-, and adeno-associated virus-mediated gene transfer to adult rodent motoneurons in vivo
Stable coculture system with established neuronal and Schwann cell lines as a valuable tool to study peripheral neuropathy
Selective localization of bone marrow-derived ramified cells in the brain adjacent to the attachments of choroid plexus
The lack of ubiquitination of the degenerated mitochondria in the spinal cord of PLA2G6 gene knockout mice
Spliceosome integrity is a common target for motor neuron disease
Prion-like properties of pathological TDP-43 aggregates in diseased brains
Prion-like spreading of pathological alpha-synuclein in brain
An autopsy case of Parkinson disease with STN-DBS
A Kii PDC patient with dopa-responsive parkinsonism followed by dementia and hallucination
Dementia with Lewy bodies with vocal cord abductor paralysis
Diffuse Lewy body disease presenting with rapidly progressive dementia: clinicopathological features in an elderly male patient
Siblings with myotonic dystrophy type 1(DM1) presenting with Lewy body pathology
An autopsy case of Lewy body disease with bilateral pallidal ischemia and clinically diagnosed as having progressive supranuclear palsy
Clinical and neuropathological study of a patient with heterozygous mutation(R94G) of PANK2
The 83 man of corticobasal degeneration who showed clinically atypical Parkinsonism and dementia
An autopsied case of unclassified 4-repeat tauopathy presenting with progressive parkinsonism
Lateralized cortical involvement and contralateral Parkinsonism in two autopsy cases of CBS-AD
Pathologoical examination in an autopsy case of familial Parkinson's disease (PARK8)
An autopsy case of 74-year-old Parkinson disease diagnosed in her twenties
Immunohistochemical analysis of autosomal recessive juvenile Parkinsonism
An autopsy case of MM2-thalamic-type sporadic Creutzfeldt-Jakob disease presenting with pure thalamic form
Investigation of the relation between the progression of cerebral cortical lesions and clinical findings in sporadic Creutzfeldt-Jakob disease
An autopsy case of familial Creutzfeldt-Jakob disease with M232R-129M/V
An autopsy Case of MM1-type sporadic Creutzfeldt-Jakob disease with a 4 years and 3 months history
Globoid cell leukodystrophy (Krabbe's disease) in a Japanese domestic cat
AD-like distribution of CBD-like pretangle neurons in an aged monkey
Pathological study of neuronal intra-cytoplasmic eosinophilic inclusion bodies (NIEIs) of Japanese Brown cattle
Neuropathology associated with left ventricular assist device: a study of 10 autopsies
Subarachnoid vasculitis in a systemic lupus erythematous patient with bacterial meningitis
An autopsy case of closed head injuries with chronic organic solvent toxicity
Crossed cerebellar atrophy resulted from different circumstances: Report of 2 cases with Review of Literature
An autopsy case of rheumatoid arthritis and other autoimmune diseases complicated by cerebral amyloid angiopathy-related inflammation
Dual compartmentalization of the so-called Virchow-Robin space in human brains into adventitial and perivascular components evidenced by cellular infiltration into them
An autopsied case of cerebral amyloid angiopathy which revealed unilateral cerebrovascular diseases after VP-shunt operation
An autopsy case of spinocerebellar ataxia 17 (SCA17) with 37 years' duration
Neuroaxonal dystrophy in dorsal column nucli in a patient with juvenile Dentatorubro-Pallidoluysian Atrophy (DRPLA)
An autopsy case of spinocerebellar ataxia type 6: Coexistence of 1C2-positive intracytoplasmic inclusions and neurofibrillary tangles within the same neurons
An autopsy case of type 6 spinocerebellar ataxia of 12 years duration
An autopsy case of SCA31 with severe dementia at terminal stage
An autopsy case of SCA31 with dorsal column degeneration
Immunohistochemical observation of L-type calcium channel in muscular disorders
Autopsy case of early onset of facioscapulohumeral dystrophy
Pathological changes of myopathy associated with anti-signal recognition particle antibody
A case of IBM with upper motor neuron sign linked to VCP p.R159H
Clinicopathological features of proximal-dominant hereditary motor and sensory neuropathy (HMSN-P) caused by TRK-fused gene (TFG) mutation
An autopsy case showing pathological findings compatible with FTLD-MND after 12-year-long history of CIDP
Congenital hypomyelinating neuropathy due to a de novo heterozygous p.Asp61Asn MPZ mutation: heterogeneous phenotypes caused by a single mutation in the MPZ gene
A case of MSA patient who presented edematous changes in medulla
An autopsy case of multiple system atrophy who died of CO2 narcosis with severe sleep apnea syndrome
An autopsy case of multiple system atrophy and Dementia with Lewy bodies, clinically autonomic dysfunction and dementia were outstanding
An autopsy case of preclinical multiple system atrophy cerebellar type
An autopsy case of hippocampal sclerosis dementia with clinical diagnosis of Alzheimer' disease
Two elderly patients with hippocampal sclerosis
Levodopa-responsive parkinsonism caused by Alzheimer-type pathology without Lewy bodies in a 85-year-old man
Pathological and biochemical study of the nucleus accumbens in tangle-predominant dementia
Case of argyrophilic grain dementia with parkinsonism clinically diagnosed as Parkinson's disease
A case of pure form argyrophilic grain dementia with psychiatric features
Corticobasal degeneration with argyrophilic grain disease: two cases showing abnormal behaviors and hallucination in the early stage
Isoform dependent intra-neuronal progression of neurofibrillary changes in Alzheimer's disease
Bipolar Disorder: clinical and pathological studies
Hereditary diffuse leukoencephalopathy with spheroids (HDLS): Histological features of microglia
A case of FTLD-TDP type A with primary lateral sclerosis presenting progressive nonfluent aphasia, anterior operculum syndrome and left pyramidal tract lesion on MRI
A case of pituitary adenoma with Rathke's cleft cysts-like component
A case of prolactin producing pituitary adenoma with extensive spherical amyloid deposition
Pineal glioblastoma presenting leptomeningeal dissemination without enlargement of the primary lesion
A case of primary central nervous system lymphoma
Primary central nervous system malignant lymphoma with multiple lesions on brain MRI
An autopsy case of primary central nervous system T-cell lymphoma
First autopsy case of Alzheimer's disease in the J-ADNI participants
Ubiquilin-1 immunoreactivity is concentrated on Hirano bodies and dystrophic neurites in Alzheimer's disease brains
The expression of neuropilin-1 in pituitary adenoma
Pleomorphic localized astrocytic tumor – report of two cases
Standardization of pathological diagnosis of brain tumors
The 75 years old autopsy case with adenocarcinoma of unknown origin, who was suspected to have venous thrombosis in MRI, and was diagnosised as venous metasitasis at autopsy
Differentiation of Alzheimer's disease and dementia with grains based on the background pathology
Evaluation of the globus pallidus lesion in progressive supranuclear palsy on magnetic resonance imaging
Primary angitis of the central nervous system
MRI findings of neuronal intranuclear hyaline inclusion disease(NIHID)-Histopathologic correlation
Familial intranuclear inclusion disease of 61-year old man in a case of brain and skin biopsies
Clinical and pathological features of adult-onset familial neuronal intranuclear hyaline inclusion disease
Intra-nuclear hyaline inclusion body disease with characteristic clinical and radiological findings which was diagnosed by Skin-Nerve-Muscle simultaneous biopsy
A case of neuronal intranuclear hyaline inclusion disease presenting polyneuropathy, episodic vomitting, neurogenic bladder dysfunction and leukoencephalopathy
A case of neuronal intranuclear hyaline inclusion disease with mitochondrial respiratory chain complex deficiencies
Case report of a patient showing leukoaraiosis after diagnosis of neuronal intranuclear inclusion disease by rectal biopsy
A case of neuronal intranuclear hyaline inclusion disease suggested by diffusion-weighted MRI and confirmed by skin biopsy
Diagnosis of Neuronal intranuclear inclusion disease with skin biopsy
Two cases of pure autonomic failure carrying out skin biopsy by different method
Alpha-synuclein accumulation in skin nerve fibers in Shy-Drager syndrome and pure autonomic failure
Usefulness of skin biopsy in the diagnosis of Lewy body diseases presenting severe autonomic dysfunctions
Lewy neurite-like structures (MSA neurite) are not associated with Lewy pathology at the brainstem of multiple system atrophy (MSA)
The relationship between atrophy and neuronal loss of basilar part of pons in multiple system atrophy (MSA)
Pathological features of axonal degeneration in multiple system atrophy
HMGB1 as a therapeutic molecule candidate for spinocerebellar ataxia type1 (SCA1)
Nuclear inclusions in SCA7 and Cajal body
A clinical and neuropathological study on two patients with spinocerebellar ataxia type 31 (SCA31)
Transmission experiment with MV2 prions
Immunohistochemical and biochemical investigation of V180I Creutzfeldt- Jakob disease with PrP positive microspheres
Immunohistochemical localization of spatacsin in alpha-synucleinopathies
Aquaporin expression and its relationship to α-synuclein/amyloid β deposition in Parkinson's disease
Park17 has both parkinson and Alzheimer pathology because of retromer impairment
Neuropathological investigation of hypocretin immunoreactivity in brains of dementia with Lewy bodies
Neuropathology underlying clinical variability in patients with Lewy body disease
Appearance of Lewy bodies in the olfactory epithelium in patients with Parkinson's disease
Report on the feasibility study for brain banking in Japan
2012 Progress report on Neruopathology Database of Tokyo Metropolitan Institute of Medical Science
Activities of the “Shinshu Brain Resource Net” in 2013
Research Resource Network Progress Report 2012
Annual report by the Nervous Disease Brain Bank
2013 Annual Report of Brain Bank for Aging Research
Newly developed “protein silver” for Bodian staining
Primary brainstem lymphoma mimicking Bickerstaff's encephalitis
An autopsy case of lymphomatoid granulomatosis
Cryptococcal choroid plexitis causing obstructive hydrocephalus in an immunocompetent patient
An autopsy case of cognitively intact centenarian
A 107-year-old autopsy case of argyrophilic grain disease and Alzheimer disease with dense neurofibrillary tangles in the hippocampal region
Neurofibrillary tangles of exclusively three-repeat tau in myotonic dystrophy
An autopsy case of front-temporal dementia with white matter degeneration
Frequencies of neurodegenerative changes in late-onset schizophrenia spectrum disorders
An autopsied case of adult-type Alexander disease with S393R mutation in the GFAP gene
An autopsy case of adult-onset Alexander disease with homozygous novel mutation in the glial fibrillary acidic protein (GFAP) gene
An autopsy case of arteriovenous malformation
An autopsy case of Vici syndrome
Bilateral peri-sylvian syndrome in a twin due to feto-fetal transfusion
An autopsy case of progressive myoclonus epilepsy (Unverricht-Lundborg disease)
A focal resection did not succeed but epileptic seizure disappeared by functional right hemispherectomy in 6 year-old girl with Rasmussen syndrome
Spectrum of so-called ‘pretangle’ of CBD on light microscopy and corresponding electron microscopic details
Significance of argyrophilic grains in Corticobasal degeneration
Autopsy-proven progressive supranuclear palsy presenting progressive freezing of gait -A clinicopathological evaluation of two PSP-PAGF cases-
Progressive supranuclear palsy (PSP) presenting pure akinesia with gait freezing -a clinicopathological study of two cases-
Long time course of midbrain atrophy over 7 years in an autopsy-confirmed PSP patient
Involvement of respiratory center of medulla oblongata in progressive supranuclear palsy: report of an autopsy case
Immunohistochemical studies of phosphorylated TDP-43 in amyotrophic lateral sclerosis (ALS) of six months' duration
An autopsy case with FTLD-MND (PLS type)
One autopsy case of Flail arm syndrome
An autopsy case of post-polio syndrome showing focal loss of spinal neurons and degeneration of the corticospinal tracts
An autopsy case of a 62-year-old woman with amyotrophic lateral sclerosis (ALS) accompanying Fused in Sarcotma (FUS)- immunoreactive basophilic inclusions
Familial amyotrophic lateral sclerosis with a novel Ala4Asp SOD1 mutation: The first neuropathological study
Neuropathologic investigation of a case with ALS and Paget disease associated with M158V VCP mutation
Neuropathological study of familial ALS cases with FUS R521C mutation
An autopsy case of familial amyotrophic lateral sclerosis with FUS R521G mutation
An autopsy case of familial amyotrophic lateral sclerosis with FUS immunoreactive inclusions
Sporadic amyotrophic lateral sclerosis with widespread multisystem degeneration in a patient after long-term survival on a respirator
An autopsy case of sporadic amyotrophic lateral sclerosis with a good communication after 28 years survival on a respirator
Non-demented ALS case with amygdala involvement without nigral lesions
MELAS with sparse stroke-like episodes and progressive diffuse brain atrophy lacking cystic necrotic lesions of cerebral cortices: an autopsy case report
Neuropathology of MELAS in the acute stage of stroke-like episode
Pathology of adult onset gangliosidosis (AOG)
An autopsy case with Chagas disease
An autopsy case of meningitis with characteristic pathological findings
The case of Sjogren syndrome with multiple infarction and multiple mass of the Brain
An autopsy case of Anti-Hu antibody positive paraneoplastic limbic encephalitis with minimal inflammatory change
Elucidation of the mechanism of activity-dependent Aβ secretion and deposition using optogenetics
The effect of nifedipine, a calcium-channel blocker, on a mouse model of subcortical vascular dementia
70-year-old female cases of encephalomyelitis after cord blood transplantation
Clasmatodendrosis in Influenza Associated Encephalopathy
An adult case of the acute encephalopathy with biphasic clinical course associated with B-cell lymphoma
HHV6 assosiated limbic encephalitis with sever skin rash after cord blood transplantation: report of an autopsy case
Encephalitis with fluctuating multiple brain lesions in a patient with human immunodeficiency virus infection
A case of the cerebellar form of progressive multifocal leukoencephalopathy in a patient under anti-retrovirus therapy for HIV infection
66-year-old man of rituximab-related progressive multifocal leukoencephalopathy showing decreased JC viral load after high dose mefloquine treatment
An autopsy case of neuromyelitis optica (NMO)
Site-related aquaporin-4 dynamics alteration in neuromyelitis optica
A clinicopathological study of familial neuromyelitis optica: a case report
An autopsy case of neuromyelitis optica (NMO) showing girdle sensation
An autopsied case suspected NMO spectrum disorder without spinal cord lesion with positive serum anti- Sjögren syndrome (SS) antibody
A case of intractable multiphasic disseminated encephalomyelitis
CD3+CD4-CD8- (double negative) T-cells infiltrate in the clinically undiagnosed idiopathic demyelinating lesions