The diagnosis of Chiari malformation is on the rise owing to the increased frequency of brain imaging for concussion and trauma. This abnormal brain physiology can have a significant impact on the care management of a pregnant woman during the gestational period. Here we present a case example of a pregnant woman presenting in labor with a history of Chiari malformation with surgical treatment during her pregnancy. Antepartum, intrapartum and postpartum considerations are reviewed. This brief article is meant to be used as an easy-reference tool in the clinical setting.