*Department of Ophthalmology, Northwestern University, Evanston, Illinois, and Departments of †Ophthalmology, ‡Pathology, and §Medicine, Baylor College of Medicine, Houstan, Texas, U.S.A.
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Abstract
Primary neuroendocrine tumors of the orbit are exceedingly rare and typically present with gradual, progressive exophthalmos. In this report, an otherwise healthy 64-year-old woman undergoes resection of a well-differentiated neuroendocrine tumor after presenting with acute proptosis. An extensive clinical and radiographic evaluation reveals no other evidence of disease, establishing the diagnosis of a primary neuroendocrine tumor. The case presentation is followed by a brief review of the classification, presentation, and evaluation of orbital neuroendocrine tumors.