BILATERAL COATS REACTION IN BANNAYAN–ZONANA SYNDROME: A SINGLE CASE REPORT

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Abstract

Purpose:

To report the clinical features of bilateral Coats reaction in a patient with Bannayan–Zonana syndrome.

Methods:

The clinical course and retinal manifestations of a 21-year-old patient with Bannayan–Zonana syndrome and bilateral Coats reaction were studied. Retinal manifestations were documented with clinical examination, ultrawide-field color imaging, and ultrawide-field fluorescein angiography.

Results:

Best-corrected visual acuities were 20/25 OD and 20/25 OS. Anterior segment examinations were normal bilaterally. The inferotemporal quadrant of the left retina demonstrated retinal telangiectasias, exudation, and a neurosensory retinal detachment extending to the mid-periphery. Fluorescein angiography demonstrated bilateral peripheral nonperfusion and vascular staining. An epiretinal membrane also involved the left macula.

Conclusion:

Bannayan–Zonana syndrome is an autosomal-dominant, hamartomatous disease characterized by a mutation spectrum that involves genes responsible for vascular development. Retinal vascular abnormalities and exudation can be a manifestation of this syndrome.

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