To present a case report of a rare ocular manifestation of Proteus syndrome—rhegmatogenous retinal detachment.Methods:
Retrospective review of the patient's medical record and a review of the literature.Results:
A 16-year-old boy with Proteus syndrome who presented with a total retinal detachment because of an operculated retinal tear. This patient underwent successful surgical repair of the retinal detachment and subsequent cataract surgery.Conclusion:
Proteus syndrome may be complicated by the development of rhegmatogenous retinal detachment, which can present in childhood.