Respiratory Failure Due to Intestinal Pseudo-obstruction in Systemic Sclerosis
We diagnosed pseudo-obstruction associated with systemic sclerosis. Interstitial pneumonia was found only slightly. She was treated with intravenous hyperalimentation and prokinetic agents, but she died of respiratory failure on the 12th day after admission.
Upward displacement of the diaphragm compresses the lungs and worsens static and dynamic pulmonary compliance, decreasing total lung capacity. This leads anatomically to basal atelectases of the lungs and, functionally, to a restrictive ventilation disorder.1,2
Fatal respiratory failure due to pseudo-obstruction of the intestine may occur in systemic sclerosis.