Giant Multilevel Thoracic Hemangioma With Spinal Cord Compression in a Patient With Klippel-Weber-Trenaunay Syndrome: Case Report

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Abstract

Study Design.

Case report and clinical discussion.

Objective.

We intend to report a very rare case of a giant spinal hemangioma causing myelopathy.

Summary of Background Data.

Multilevel symptomatic spinal hemangiomas causing acute neurologic symptoms are rare disorders. We found only sporadic reports in English literature.

Methods.

We describe a very rare case in which Klippel-Trenaunay-Weber syndrome is associated with a multisegmental vertebral hemangioma causing a rapidly progressing thoracic myelopathy.

Results.

Because of the extension of the disease, surgical intervention was not feasible, the patient was treated by radiotherapy. The patient showed a complete regression of symptoms with stable condition after 3 months.

Conclusions.

In extensive spinal hemangiomas, radiotherapy may represent a safe treatment modality with rapid clinical improvement even in cases with spinal cord compression. This report contributes to a wide range of known vascular abnormalities in Klippel-Trenaunay-Weber syndrome and supports the need for a careful multisystemic evaluation of these patients.

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